The Mucopolysaccharidoses as Lysosomal Diseases

  • F Van Hoof
  • H. G. Hers
Part of the Advances in Experimental Medicine and Biology book series (AEMB, volume 19)

Abstract

In this paper, we briefly summarize the evidence that has accumulated during the recent years indicating that the diseases known as mucopolysaccharidoses are due to the primary defect of one acid hydrolase normally present in lysosomes.

Keywords

Kupffer Cell Acid Hydrolase Lysosomal Hydrolase Cholesterol Sulfate Lysosomal Disease 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer Science+Business Media New York 1972

Authors and Affiliations

  • F Van Hoof
    • 1
  • H. G. Hers
    • 1
  1. 1.Laboratoire de Chimie PhysiologiqueUniversité de LouvainLouvainBelgium

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