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Systemic Vasculitis Syndromes

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Part of the Comprehensive Manuals in Pediatrics book series (CM PEDIATRICS)

Abstract

Vasculitis, inflammation in and around the blood vessels, which is sometimes associated with fibrinoid necrosis, may be seen in many of the conditions discussed in this book. In most rheumatic diseases, vasculitis is only one feature of a well-defined, complex, pathologic process (Fig. 7.1), and the disease (e.g., SLE or dermatomyositis) is best characterized by other distinctive diagnostic clinical and laboratory features. However, in the diverse and perhaps totally unrelated syndromes discussed in this chapter, vasculitis itself is the predominant pathologic process, and the clinical manifestations are primarily a direct result of the damage to the blood vessels (Table 7.1).

Keywords

  • Kawasaki Disease
  • Systemic Vasculitis
  • Polyarteritis Nodosa
  • Coronary Artery Aneurysm
  • Mixed Cryoglobulinemia

These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Jacobs, J.C. (1982). Systemic Vasculitis Syndromes. In: Pediatric Rheumatology for the Practitioner. Comprehensive Manuals in Pediatrics. Springer, New York, NY. https://doi.org/10.1007/978-1-4757-6153-5_7

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