Disorders of Female Sex Differentiation

  • Lawrence R. Shapiro

Abstract

This chapter deals with disturbances of female sex differentiation during embryogenesis and the resulting disorders of genetic, gonadal, and phenotypic sex. Because the embryologic details have been discussed in another chapter, they are only briefly reviewed. An understanding of the pathogenesis of abnormal sexual differentiation is essential as a basis of diagnosis and ultimate therapy.

Keywords

Congenital Adrenal Hyperplasia Turner Syndrome Gonadal Dysgenesis Male Pseudohermaphroditism Testicular Feminization 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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  • Lawrence R. Shapiro

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