Abstract
A study dedicated to research of tryptophan and its metabolites in urine of Hartnup disease was published 30 years ago (Milne et al., 1960). The present paper pertains to the investigation of L-tryptophan (TRY), kynurenine (KYN), xanthurenic acid (XA), 5-hydroxyindoleacetic acid (5-HIAA) and indoxyl sulfate (IS) in plasma and urine of a four member family, with one symptomatic and one asymptomatic patient with Hartnup disease, prior to and after a TRY load. In parallel, one healthy subject was studied.
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© 1991 Plenum Press, New York
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Milovanović, D.D., Milovanović, L., Stanković, B., Radulović, D. (1991). Tryptophan and its Metabolites in a Family with Hartnup Disease. In: Schwarcz, R., Young, S.N., Brown, R.R. (eds) Kynurenine and Serotonin Pathways. Advances in Experimental Medicine and Biology, vol 294. Springer, Boston, MA. https://doi.org/10.1007/978-1-4684-5952-4_90
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DOI: https://doi.org/10.1007/978-1-4684-5952-4_90
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