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Cystic Fibrosis

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Clinical Disorders of Membrane Transport Processes

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Abstract

Cystic fibrosis, an apparent inborn error of metabolism, is a common disease of children and young adults in countries with predominantly Caucasian populations. It was first described by Fanconi et al. in Switzerland following the recognition of the association of congenital cystic pancreatic fibrosis and bronchiectasis in 1936.(1) In this country, it was Andersen(2) who presented in 1938 the first complete description of the disease and introduced the term “cystic fibrosis of the pancreas.” Although other names for the disease have been proposed in the past decades,(3,4) the shortened form of the original name for the disease, “cystic fibrosis,” has become most common. Several detailed reviews have recently appeared in the literature.(3–6)

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Authors and Affiliations

  1. Department of Pediatrics, University of Texas Health Science Center, San Antonio, Texas, 78284, USA

    John A. Mangos

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  1. John A. Mangos
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Editor information

Editors and Affiliations

  1. Department of Internal Medicine, University of Texas Medical School, 77225, Houston, Texas, USA

    Thomas E. Andreoli M.D. (Edward Randall III Professor and Chairman, Professor of Physiology and Cell Biology) (Edward Randall III Professor and Chairman, Professor of Physiology and Cell Biology)

  2. Yale University School of Medicine, New Haven, Connecticut, USA

    Joseph F. Hoffman Ph.D.

  3. University of California, San Diego, La Jolla, California, USA

    Darrell D. Fanestil M.D.

  4. University of Texas Medical School, Houston, Texas, USA

    Stanley G. Schultz M.D.

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© 1987 Plenum Publishing Corporation

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Mangos, J.A. (1987). Cystic Fibrosis. In: Andreoli, T.E., Hoffman, J.F., Fanestil, D.D., Schultz, S.G. (eds) Clinical Disorders of Membrane Transport Processes. Springer, Boston, MA. https://doi.org/10.1007/978-1-4684-1286-4_9

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  • DOI: https://doi.org/10.1007/978-1-4684-1286-4_9

  • Publisher Name: Springer, Boston, MA

  • Print ISBN: 978-0-306-42699-5

  • Online ISBN: 978-1-4684-1286-4

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