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Phenylketonuria: Biochemical Mechanisms

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Advances in Neurochemistry

Part of the book series: Advances in Neurochemistry ((CORG,volume 2))

Abstract

As implied by the title, this review of phenylketonuria (PKU) will be neither comprehensive nor encyclopedic. Rather, it will be limited to those aspects of the disease where sufficient biochemical knowledge is available to support meaningful discussion—admittedly, often speculative—about underlying mechanisms. Recent comprehensive reviews are available (Hsia, 1970; Knox, 1972).

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Authors and Affiliations

  1. Laboratory of Neurochemistry, National Institute of Mental Health, Bethesda, Maryland, USA

    Seymour Kaufman

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  1. Seymour Kaufman
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  1. Mental Health Research Institute and Department of Biological Chemistry, University of Michigan, Ann Arbor, Michigan, USA

    B. W. Agranoff

  2. Institute of Psychiatric Research and Department of Psychiatry and Biochemistry, Indiana University School of Medicine, Indianapolis, Indiana, USA

    M. H. Aprison

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© 1977 Plenum Press, New York

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Kaufman, S. (1977). Phenylketonuria: Biochemical Mechanisms. In: Agranoff, B.W., Aprison, M.H. (eds) Advances in Neurochemistry. Advances in Neurochemistry, vol 2. Springer, Boston, MA. https://doi.org/10.1007/978-1-4615-8237-3_1

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  • DOI: https://doi.org/10.1007/978-1-4615-8237-3_1

  • Publisher Name: Springer, Boston, MA

  • Print ISBN: 978-1-4615-8239-7

  • Online ISBN: 978-1-4615-8237-3

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