Abstract
Cystic fibrosis (CF) affects a number of epithelial-lined organs, the most important being the lungs, responsible for the majority of the morbidity in this disease and eventually the usual cause of death from respiratory failure. This lung disease results from impaired airway defence against infection; bacterial colonisation usually occurs in childhood and progresses to episodes of overt infection and subsequent lung damage.
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Alton, E.W.F.W. (1996). Gene Delivery and Therapy: The Case for Cystic Fibrosis. In: Gregoriadis, G., McCormack, B. (eds) Targeting of Drugs 5. NATO ASI Series, vol 290. Springer, Boston, MA. https://doi.org/10.1007/978-1-4615-6405-8_2
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DOI: https://doi.org/10.1007/978-1-4615-6405-8_2
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