Cortical Dysgenesis in Adults with Epilepsy
Gross cortical dysgenesis (CD) is a well-recognised cause of epilepsy. Affected patients present with epilepsy in infancy or early childhood, are often severely mentally handicapped, and more often than not exhibit bilateral motor deficits. Recently, subtle forms of CD have been identified in adults with previously designated cryptogenic epilepsy (Raymond et al., 1992, 1993). Unlike children with CD, affected adults may have normal intelligence and rarely exhibit fixed neurological signs.
KeywordsTuberous Sclerosis Focal Cortical Dysplasia Germinal Matrix Dysembryoplastic Neuroepithelial Tumour Multiplanar Reformat
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