Surgery for West’s Syndrome

  • Harold J. Hoffman
Part of the Advances in Experimental Medicine and Biology book series (AEMB, volume 497)


West’s syndrome or “infantile spasms” is named after a physician by the name of West, who wrote a letter to Lancet in 1841 in which he described a “peculiar form of convulsion” associated with mental retardation as seen in his son. Clinically, West’s syndrome consists of a triad of myoclonic spasms, hypsarrhythmic EEG and mental retardation.


Tuberous Sclerosis Focal Cortical Dysplasia Infantile Spasm Cortical Dysplasia Intractable Seizure 
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Copyright information

© Springer Science+Business Media New York 2002

Authors and Affiliations

  • Harold J. Hoffman
    • 1
  1. 1.Division of Neurosurgery The Hospital for Sick Children ProfessorDepartment of Surgery University of TorontoCanada

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