Genetic Polymorphisms and Their Role in Ventricular Arrhythmias

  • S. Kääb
  • M. Näbauer
  • A. Pfeufer
Part of the Developments in Cardiovascular Medicine book series (DICM, volume 242)


Potentially life threatening ventricular arrhythmias may occur as a consequence of genetic variants affecting key proteins that directly or indirectly alter myocardial electrical properties. Diseases such as Long-QT-Syndrome, Brugada Syndrome, catecholaminergic polymorphic ventricular tachycardia in structurally normal hearts and hypertrophic, dilated, and right ventricular cardiomyopathy in structurally abnormal hearts are the best known examples of monogenic conditions causing ventricular arrhythmias and sudden cardiac death (SCD).


Ventricular Arrhythmia Brugada Syndrome Right Bundle Branch Block Ventricular Cardiomyopathy Arrhythmogenic Right Ventricular Dysplasia 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.


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Copyright information

© Springer Science+Business Media New York 2002

Authors and Affiliations

  • S. Kääb
  • M. Näbauer
  • A. Pfeufer

There are no affiliations available

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