Decision Analysis Strategies for HLHS: Orthotopic Heart Transplantation vs. Staged Palliation

  • Bernard J. ClarkIII
Part of the Developments in Cardiovascular Medicine book series (DICM, volume 246)


The scenario is all too familiar to the practicing pediatric cardiologist. It is something we should do well. An infant is born, recognized to be ill, and an echocardiogram is performed. The diagnosis of HLHS is made. The parents and family are now being told the details of their child’s diagnosis and possible treatment. Three options are offered to the family: 1) allowing the infant to die of its disease 2) to undergo heart transplantation or 3) to undergo a series of operations over the next 2 years leading to a Fontan procedure.


Congenital Heart Disease Hypoplastic Left Heart Syndrome Late Death Fontan Procedure Orthotopic Heart Transplantation 
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Copyright information

© Springer Science+Business Media New York 2003

Authors and Affiliations

  • Bernard J. ClarkIII
    • 1
  1. 1.Division of CardiologyThe Children’s Hospital of PhiladelphiaUSA

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