Abstract
The scenario is all too familiar to the practicing pediatric cardiologist. It is something we should do well. An infant is born, recognized to be ill, and an echocardiogram is performed. The diagnosis of HLHS is made. The parents and family are now being told the details of their child’s diagnosis and possible treatment. Three options are offered to the family: 1) allowing the infant to die of its disease 2) to undergo heart transplantation or 3) to undergo a series of operations over the next 2 years leading to a Fontan procedure.
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Clark, B.J. (2003). Decision Analysis Strategies for HLHS: Orthotopic Heart Transplantation vs. Staged Palliation. In: Rychik, J., Wernovsky, G. (eds) Hypoplastic Left Heart Syndrome. Developments in Cardiovascular Medicine, vol 246. Springer, Boston, MA. https://doi.org/10.1007/978-1-4615-0253-1_20
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DOI: https://doi.org/10.1007/978-1-4615-0253-1_20
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