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Cardiac Structure And Function After Staged Reconstruction

  • Chapter
Hypoplastic Left Heart Syndrome

Part of the book series: Developments in Cardiovascular Medicine ((DICM,volume 246))

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Abstract

In hypoplastic left heart syndrome (HLHS) the tricuspid valve functions as the systemic atrioventricular valve. It has been suggested that the structure of the tricuspid valve makes more likely to leak in the setting of systemic pressure in the right ventricle. Van Praagh et al. have argued that the mitral valve is much better designed to occlude an approximately circular systemic atrioventricular orifice [1]. However, in a recent retrospective analysis of 531 patients with single ventricle who underwent staged palliation, we found no significant difference in the prevalence of regurgitation between the mitral or tricuspid valve (previously unpublished data).

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Author information

Authors and Affiliations

  1. Sibley Heart Center, Children’s Healthcare OF Atlanta, USA

    William Mahle M.D.

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  1. William Mahle M.D.
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Editors and Affiliations

  1. Division of Cardiology, Children’s Hospital of Philadelphia, Philadelphia, USA

    Jack Rychik M.D.  & Gil Wernovsky M.D.  & 

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Mahle, W. (2003). Cardiac Structure And Function After Staged Reconstruction. In: Rychik, J., Wernovsky, G. (eds) Hypoplastic Left Heart Syndrome. Developments in Cardiovascular Medicine, vol 246. Springer, Boston, MA. https://doi.org/10.1007/978-1-4615-0253-1_16

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  • DOI: https://doi.org/10.1007/978-1-4615-0253-1_16

  • Publisher Name: Springer, Boston, MA

  • Print ISBN: 978-1-4613-4988-4

  • Online ISBN: 978-1-4615-0253-1

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