Aortic Arch Anomalies

  • Scott DeRoo
  • Jonathan R. Dillman
  • Philip Cascade
  • Richard G. Ohye
  • Baskaran Sundaram


Congenital anomalies of the aortic arch represent a diverse set of malformations with a common embryologic origin and a wide array of clinical manifestations. Arch anomalies are noted in 1–10/1,000 live births and account for approximately 15–20 % of all congenital heart disease (Hoffman and Kaplan, J Am Coll Cardiol 39:1890–1900, 2002). Presentation of aortic arch anomalies is highly variable with many patients remaining asymptomatic throughout life. When present, symptoms generally result from compression of surrounding mediastinal structures or associated intracardiac defects. Successful management of symptomatic arch anomalies often relies on surgical or endovascular intervention aimed at relieving compression or improving hemodynamics. In this review, we present several common aortic anomalies in correlation with their embryologic development and clinical features.


Aortic Arch Subclavian Artery Left Subclavian Artery Aortic Coarctation Vascular Ring 
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Copyright information

© Springer Science+Business Media New York 2014

Authors and Affiliations

  • Scott DeRoo
    • 1
  • Jonathan R. Dillman
    • 2
  • Philip Cascade
    • 3
  • Richard G. Ohye
    • 4
  • Baskaran Sundaram
    • 5
  1. 1.Division of Cardiothoracic SurgeryColumbia UniversityNew YorkUSA
  2. 2.Department of RadiologyUniversity of Michigan Health SystemAnn ArborUSA
  3. 3.Division of Cardiothoracic Radiology, Department of RadiologyUniversity of Michigan Health SystemAnn ArborUSA
  4. 4.Department of Cardiac SurgeryUniversity of Michigan Health SystemAnn ArborUSA
  5. 5.Division of Cardiothoracic Radiology, Department of RadiologyUniversity of Michigan Health System, Cardiovascular Center 5481Ann ArborUSA

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