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Cardiac CT and MR Evaluation of the Adult Fontan Patient

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Cardiac CT and MR for Adult Congenital Heart Disease

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Abstract

Congenital heart disease resulting in single ventricular physiology includes many diverse diagnoses (see Table 21.1). Optimal palliation for such patients requires that the ventricle act as the systemic pump and that a secure source of pulmonary blood flow is created. Unobstructed flow to the systemic and pulmonary circulations is the goal; optimally, widely patent aortic anatomy and branch pulmonary arteries are desirable. Due to complex anatomy and hemodynamics, any single ventricle patient with Fontan palliation requires continued meticulous medical surveillance. A critical component of this care involves advanced cardiac imaging. A multimodality imaging approach for the Fontan patient is best performed at a center with expertise in adult congenital heart disease and in-depth knowledge regarding the advantages and disadvantages of each imaging technique. Cardiac magnetic resonance (CMR) imaging and multidetector cardiac computed tomography (MDCT) are the noninvasive, advanced cardiac imaging techniques presented here.

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Author information

Authors and Affiliations

  1. Section of Pediatric Cardiology, Riley Hospital for Children, Indiana University, 705 Riley Hospital Drive, Riley Research Rm 127, Indianapolis, IN, 46202-5225, USA

    Tiffanie R. Johnson MD, FAAP, FACC

  2. Pediatric Cardiology, The Herma Heart Center, Children’s Hospital of Wisconsin, Medical College of Wisconsin, 9000 West Wisconsin Avenue, Milwaukee, WI, 53226, USA

    Margaret M. Samyn MD, FAAP, FACC

  3. Department of Radiology, Boston Children’s Hospital, Harvard Medical School, 300 Longwood Ave, Boston, MA, 02115, USA

    Laureen Sena MD

Authors
  1. Tiffanie R. Johnson MD, FAAP, FACC
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  2. Margaret M. Samyn MD, FAAP, FACC
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  3. Laureen Sena MD
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Corresponding author

Correspondence to Tiffanie R. Johnson MD, FAAP, FACC .

Editor information

Editors and Affiliations

  1. Department of Radiology, USC University Hospital Keck School of Medicine, Los Angeles, California, USA

    Farhood Saremi

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Johnson, T.R., Samyn, M.M., Sena, L. (2014). Cardiac CT and MR Evaluation of the Adult Fontan Patient. In: Saremi, F. (eds) Cardiac CT and MR for Adult Congenital Heart Disease. Springer, New York, NY. https://doi.org/10.1007/978-1-4614-8875-0_21

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  • DOI: https://doi.org/10.1007/978-1-4614-8875-0_21

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