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Critical and Respiratory Care in Neuromuscular Disorders

Chapter

Abstract

Critical care of patients with neuromuscular disease has evolved over the years to include diagnosis, recognition, and management of the natural progression of these disorders as well as the treatments, potential side effects, and comorbid illnesses that are often seen in the intensive care units. In this chapter, we discuss the general critical care approach, the basic changes in pulmonary function, the electrodiagnostic testing, and the pulmonary aspects of the neuromuscular disorders seen in the ICU. We also discuss long-term respiratory care and management of chronic respiratory failure since it constitutes an essential aspect of medical care in patients with progressive neuromuscular diseases.

Keywords

muscular dystrophy Malignant hyperthermia Acid maltase deficiency Periodic paralysis myasthenia gravis inspiratory force vital capacity pulmonary function tests 

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Copyright information

© Springer Science+Business Media New York 2014

Authors and Affiliations

  1. 1.Department of NeurologyMedical College of Wisconsin and Froedtert HospitalMilwaukeeUSA
  2. 2.Division of Pulmonary/Critical Care and Sleep Medicine, Department of MedicineUniversity Hospital Case Medical Center, Case Western Reserve University School of MedicineClevelandUSA
  3. 3.Department of NeurologyBaylor College of MedicineHoustonUSA

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