Clear Cell Sarcoma/Melanoma of Soft Parts
Is it a sarcoma or is it a melanoma? Clear cell sarcoma (CCS), also called clear cell sarcoma of tendons and aponeuroses [1, 2], has features of both. CCS represents perhaps 1 % of all sarcomas. Since it starts in soft tissue and usually does not affect skin , CCS is anatomically distinct from melanoma. Patients are typically younger, between 15 and 45 years of age, and women are more commonly affected than men. The foot and ankle are common primary locations for this rare sarcoma. Age and site distribution for adult patients are shown in Figs. 18.1 and 18.2.
KeywordsTyrosine Sarcoma Sunitinib Ifosfamide Histiocytoma
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