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Rasmussen’s Syndrome

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Epilepsy
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Abstract

Rasmussen’s syndrome is a childhood developing syndrome, usually characterized by refractory focal motor seizures (epilepsia partialis continua). Most cases originate between the age of 1 and 10 years, mean age about 5 years. Symptoms are attributed to chronic pathogen-free inflammation of both gray and white matter. There is a progressive unihemispheric atrophy (Rasmussen 1978). In 50% of patients, the onset of Rasmussen encephalitis is preceded by an inflammatory episode such as an U.R.I.

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McCandless, D.W. (2012). Rasmussen’s Syndrome. In: Epilepsy. Springer, New York, NY. https://doi.org/10.1007/978-1-4614-0361-6_22

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