Skip to main content
SpringerLink
Log in

Proximal Femoral Focal Deficiency

  • Chapter
Congenital Lower Limb Deficiencies

Abstract

Congenital abnormalities of the femur with or without involvement of the hip joint are numerous and have been widely reported in the literature. Among them is a group of conditions involving primarily the subtrochantric area of the proximal femur. The rest of the femur and iliofemoral articulation are involved to a certain degree as well. These conditions have a rather distinct clinical and radiographic appearance.

This is a preview of subscription content, log in via an institution to check access.

Access this chapter

Log in via an institution
Chapter
USD 29.95
Price excludes VAT (USA)
  • Available as PDF
  • Read on any device
  • Instant download
  • Own it forever
eBook
USD 84.99
Price excludes VAT (USA)
  • Available as EPUB and PDF
  • Read on any device
  • Instant download
  • Own it forever
Softcover Book
USD 109.99
Price excludes VAT (USA)
  • Compact, lightweight edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info

Tax calculation will be finalised at checkout

Purchases are for personal use only

Institutional subscriptions

Preview

Unable to display preview. Download preview PDF.

Unable to display preview. Download preview PDF.

References

  1. Aitken GT: Amputation as a treatment for certain lower-extremity congenital abnormalities. J Bone Joint Surg Am 41-A: 1267–1285, 1959.

    PubMed  Google Scholar 

  2. Aitken GT: Proximal femoral deficiency, in: Limb Development and Deformity: Problems of Evaluation and Rehabilitation, Springfield II, Charles C Thomas Publisher, 1969.

    Google Scholar 

  3. Aitken GT: Proximal femoral deficiency. Definition, classification and management, in: A Symposium on Proximal Femoral Focal Deficiency—A Congenital Anomaly. National Academy of Sciences, 1969.

    Google Scholar 

  4. Amstutz HC, Wilson PD Jr: Dysgenesis of the proximal femur (coxa vara) and its surgical management. J Bone Joint Surg Am 44-A: 1–24, 1962.

    PubMed  Google Scholar 

  5. Amstutz HC: The morphology, natural history, and treatment of proximal femoral focal deficiency, in: A Symposium on Proximal Femoral Focal Deficiency—A Congenital Anomaly. National Academy of Sciences, 1969.

    Google Scholar 

  6. Badger VM, Lambert CN: Differential diagnosis of an apparent proximal femoral focal deficiency. InterClin Inform Bull 5(1): 3, 1965, New York: Committee on Prosthetic Research and Development.

    Google Scholar 

  7. Bevan-Thomas WH, Millar E-A: A review of proximal focal femoral deficiencies. J Bone Joint Surg Am 49-A: 1378, 1967.

    Google Scholar 

  8. Bochmann D. Prosthetic devices for the management of proximal femoral focal deficiency. Ortho-Pros 1980: 4.

    Google Scholar 

  9. Borggreve J: Kniegelenksersatz durch das in der Beinlangachse um 180 degree gedrehte Fussgelenk. Arch Orthop Chir 28: 175–178, 1930.

    Article  Google Scholar 

  10. Burgess E: The surgical means of obtaining hip stability with motion in congenital proximal femoral focal deficiency. InterClin Inform Bull 1(3): 1, 1961, New York: Committee on Prosthetic Research and Development.

    Google Scholar 

  11. Epps CH Jr: Proximal femoral focal deficiency J Bone Joint Surg Am 65-A: 867–870, July 1983.

    Google Scholar 

  12. Fixsen JA, Lloyd-Roberts GC: The natural history and early treatment of proximal femoral dysplasia. J Bone Joint Surg Am: 56-B: 86–95, 1974.

    CAS  Google Scholar 

  13. Gillespie R, Torode IP: Classification and management of congenital abnormalities of the femur, J Bone Joint Surg Am 65-B, No 5, 557–568, 1983.

    Google Scholar 

  14. Hall JE: Rotation of congenitally hypoplastic lower limbs to use the ankle joint as a knee. InterClin Inform Bull 6(2): 3, 1966, New York: Committee on Prosthetic Research and Development.

    Google Scholar 

  15. Hall JE, Bochmann D: The surgical and prosthetic management of proximal femoral focal deficiency, in: A Symposium: Proximal Femoral Focal Deficiency—A Congenital Anomaly. National Academy of Sciences, 1969.

    Google Scholar 

  16. Hamanishi C: Congenital short femur: clinical, genetic and epidemiological comparison of the naturally occuring condition with that caused by Thalidomide. J Bone Joint Surg Am 62-B 307–320, 1980.

    CAS  Google Scholar 

  17. Hussain T, Emmerson A: Conservative management of bilateral proximal femoral focal deficiency. InterClin Inform Bull 13(9): 9, 1974, New York: Committee on Prosthetic Research and Development.

    Google Scholar 

  18. Kalamchi A, Cowell HR, Kim KI: Congenital deficiency of the femur. J Pediatr Orthop 5: 129–134, 1985.

    PubMed  CAS  Google Scholar 

  19. King RE: Concepts of proximal femoral focal deficiencies. InterClin Inform Bull 1(2): 1, 1961, New York: Committee on Prosthetic Research and Development.

    Google Scholar 

  20. King RE: Surgical correction of proximal femoral focal deficiency. InterClin Inform Bull 4(11): 1, 1965, New York: Committee on Prosthetic Research and Development.

    Google Scholar 

  21. King RE: Providing a single skeletal lever in proximal femoral focal deficiency. InterClin Inform Bull 6(2):23, 1966, New York: Committee on Prosthetic Research and Development.

    Google Scholar 

  22. King RE: Some concepts of proximal femoral focal deficiency, in: A Symposium: Proximal Femoral Focal Deficiency—A Congenital Anomaly. National Academy of Sciences, 1969.

    Google Scholar 

  23. King RE, McCraney T: Proximal femoral focal deficiency—Quo vadis? InterClin Inform Bull 12(8): 1, 1973, New York: Committee on Prosthetic Research and Development.

    Google Scholar 

  24. King RE, Marks TW: Follow-up findings on the skeletal lever in the surgical management of proximal femoral focal deficiency. InterClin Inform Bull 11(3): 1, 1971, New York: Committee on Prosthetic Research and Development.

    Google Scholar 

  25. Korman LA, Meyer LC, Warren FH: Proximal femoral focal deficiency: A 50-year experience. Dev Med Child Neurol 24: 344, 1982.

    Article  Google Scholar 

  26. Kostuik JP, Gillespie R, Hall JE, et al: Van Nes rotational osteotomy for treatment of proximal femoral focal deficiency and congenital short femur. J Bone Joint Surg 57-A: 1039, 1975.

    PubMed  CAS  Google Scholar 

  27. A. Kritter AE: Tibial rotation-plasty for proximal femoral focal deficiency. J Bone Joint Surg 59-A: 927, 1977.

    PubMed  CAS  Google Scholar 

  28. Kritter AE, Gillespie T: Bilateral proximal femoral focal deficiency and bilateral paraxial fibular hemimelia. InterClin Inform Bull 11(12): 1, 1972, New York: Committee on Prosthetic Research and Development.

    Google Scholar 

  29. Lloyd-Roberts GC, Stone KH: Congenital hypoplasia of the upper femur. J Bone Joint Surg 45-B: 557, 1963.

    CAS  Google Scholar 

  30. Marotz RJ: Pregnancy and maternal proximal focal femoral deficiency. A case report. J Reprod Med 28 (11): 798–800, 1983.

    PubMed  CAS  Google Scholar 

  31. Meyer LC, Friddle D, Pratt RW: Problems of treating and fitting the patient with proximal femoral focal deficiency. InterClin Inform Bull 10(12): 1, 1971, New York: Committee on Prosthetic Research and Development.

    Google Scholar 

  32. Morgan JD, Somerville EW: Normal and abnormal growth at the upper end of the femur. J Bone Joint Surg 42-B: 264, 1960.

    Google Scholar 

  33. O’Rahilly R: Normal development of the human embryo, in: Normal and Abnormal Embryologic Development. National Research Council. 1967.

    Google Scholar 

  34. Panting AL, Williams PF: Proximal femoral focal deficiency. J Bone Joint Surg 60-B: 46, 1978.

    CAS  Google Scholar 

  35. Steel Howard H, Lin Paul S, Betz Randal R, et al: Iliofemoral fusion for proximal femoral focal deficiency. J Bone Joint Surg 69-A, 6 (July), 1987.

    Google Scholar 

  36. Van Nes CP: Rotation-plasty for congenital defects of the femur. Making use of the ankle of the shortened limb to control the knee joint of a prosthesis. J Bone Joint Surg 32-B: 12, 1950.

    Google Scholar 

  37. Wagner H: Operative Beinverlangerung. Chirurg 42: 260, 1971.

    PubMed  CAS  Google Scholar 

  38. Wenzlaff EF: Surgical ablation of the remaining femoral segment in proximal femoral focal deficiency. InterClin Inform Bull 9(1): 1, 1969, New York: Committee on Prosthetic Research and Development.

    Google Scholar 

  39. Westin GW, Gunderson GO: Proximal femoral focal deficiency—A review of treatment experiences. In deficiency—A review of treatment experiences, in: A Symposium on Proximal Femoral Focal Deficiency—A Congenital Anomaly. National Academy of Sciences, 1969.

    Google Scholar 

Download references

Authors
  1. Ivan Krajbich
    View author publications

    You can also search for this author in PubMed Google Scholar

Editor information

Editors and Affiliations

  1. Limestone Medical Center, Suite 209, 19808, Wilmington, DE, USA

    Ali Kalamchi M.D., F.A.C.S., F.R.C.S.

Rights and permissions

Reprints and permissions

Copyright information

© 1989 Springer-Verlag New York Inc.

About this chapter

Cite this chapter

Krajbich, I. (1989). Proximal Femoral Focal Deficiency. In: Kalamchi, A. (eds) Congenital Lower Limb Deficiencies. Springer, New York, NY. https://doi.org/10.1007/978-1-4613-8882-1_6

Download citation

  • DOI: https://doi.org/10.1007/978-1-4613-8882-1_6

  • Publisher Name: Springer, New York, NY

  • Print ISBN: 978-1-4613-8884-5

  • Online ISBN: 978-1-4613-8882-1

  • eBook Packages: Springer Book Archive

Publish with us

Policies and ethics

Search

Navigation