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Vasculitic Diseases of the Kidney

  • Chapter
Therapy of Renal Diseases and Related Disorders

Abstract

Systemic diseases associated with inflammatory and necrotizing lesions of blood vessels, ranging from muscular arteries to glomerular capillaries to dermal venules, produce major diagnostic as well as therapeutic challenges to the clinician. Few medical conditions present as diversely both in regard to renal and extra-renal manifestations. Kussmaul and Maier in 1866 originally described a young patient with Bright’s disease and progressive muscular weakness who at autopsy exhibited nodular swelling of arteries, a condition they termed, periarteritis nodosa (1). It subsequently became evident that classical periarteritis nodosa was relatively rare, but the related name, polyarteritis nodosa, became widely accepted to describe a wide variety of vasculitic diseases. Currently, the synonomous term, systemic necrotizing vasculitis, is generally preferred since it can be more appropriately applied to vasculitic diseases with and without nodular vascular lesions.

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Authors
  1. James E. Balow
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  2. Howard A. Austin III
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Editor information

Editors and Affiliations

  1. The Bernard J. Hanley, Los Angeles, CA, 90033, USA

    Wadi N. Suki M.D. (Professor of Medicine Professor of Physiology and Biophysics Chief) (Professor of Medicine Professor of Physiology and Biophysics Chief)

  2. Division of Nephrology, University of Southern California School of Medicine, Los Angeles, CA, 90033, USA

    Wadi N. Suki M.D. (Professor of Medicine Professor of Physiology and Biophysics Chief) (Professor of Medicine Professor of Physiology and Biophysics Chief)

  3. Renal Section Baylor College of Medicine, The Methodist Hospital, Houston, TX, 77030, USA

    Shaul G. Massry M.D. (Professor of Medicine and Physiology Chief) (Professor of Medicine and Physiology Chief)

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© 1984 Martinus Nijhoff Publishers, Boston / The Hague / Dordrecht / Lancaster

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Balow, J.E., Austin, H.A. (1984). Vasculitic Diseases of the Kidney. In: Suki, W.N., Massry, S.G. (eds) Therapy of Renal Diseases and Related Disorders. Springer, Boston, MA. https://doi.org/10.1007/978-1-4613-3807-9_20

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  • DOI: https://doi.org/10.1007/978-1-4613-3807-9_20

  • Publisher Name: Springer, Boston, MA

  • Print ISBN: 978-1-4613-3809-3

  • Online ISBN: 978-1-4613-3807-9

  • eBook Packages: Springer Book Archive

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