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Computed Tomography of Congenital Brain Malformations pp 50–76Cite as

Holoprosencephaly (Prosencephaly)

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Abstract

Initially described by Rudius in 1588 (4), holoprosencephaly comprises malformation of the brain and the face. Arhinencephaly, the original name coined by Kundrat in 1882 (5), is not appropriate since it implies maldevelopment of only the olfactory bulbs and tracts, whereas this disorder involves almost all supratentorial compartment structures.

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Authors and Affiliations

  1. Section of Neuroradiology, Yale University School of Medicine, New Haven, CT, USA

    Mohammad Sarwar M.D. (Associate Professor of Diagnostic Radiology)

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  1. Mohammad Sarwar M.D.
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© 1985 Warren H. Green, Inc.

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Sarwar, M. (1985). Holoprosencephaly (Prosencephaly). In: Computed Tomography of Congenital Brain Malformations. Springer, Boston, MA. https://doi.org/10.1007/978-1-4613-2571-0_4

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  • DOI: https://doi.org/10.1007/978-1-4613-2571-0_4

  • Publisher Name: Springer, Boston, MA

  • Print ISBN: 978-1-4612-9614-0

  • Online ISBN: 978-1-4613-2571-0

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