The Cellular Basis of the Pathophysiology and Treatment of Pulmonary Hypertension

  • Stuart Rich
Part of the NATO ASI Series book series (NSSA, volume 281)


Pulmonary hypertension has traditionally been categorized into primary and secondary types. Although primary pulmonary hypertension (PPH) is felt to be relatively unique as a cardiopulmonary disease, its distinction from secondary forms of pulmonary hypertension often solely depends on whether or not an identifiable etiology can be ascertained. Histologically it can be impossible to distinguish primary from secondary forms of pulmonary hypertension (Pietra et al, 1989), suggesting that the distinction may be in the mechanism(s) that produce the pulmonary vascular disease with pulmonary hypertension as a common end point.


Pulmonary Hypertension Congenital Heart Disease Pulmonary Blood Flow Primary Pulmonary Hypertension Secondary Form 
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Copyright information

© Plenum Press, New York 1996

Authors and Affiliations

  • Stuart Rich
    • 1
  1. 1.University of Illinois at Chicago Section of Cardiology (M/C 787)ChicagoUSA

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