Abstract
Retinitis pigmentosa is a progressive primary pigmentary dystrophy of the retina characterized by a collection of bone spicule-shaped pigment located in the midperiphery of the retina, a marked narrowing of the retinal arterioles, night blindness, altered dark adaptation, a diminished electroretinogram, and constricted visual fields (ring scotomas). The retinal veins appear normal in retinitis pigmentosa, as do the optic nerve heads and the maculae initially. However, as the disease progresses, optic pallor (waxy) usually will develop and in some cases cystoid macular edema with macular atrophy also will be present.
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© 1988 Keith M. Zinn and Springer-Verlag New York Inc.
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Zinn, K.M. (1988). Retinitis Pigmentosa. In: Clinical Atlas of Peripheral Retinal Disorders. Springer, New York, NY. https://doi.org/10.1007/978-1-4612-3720-4_11
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DOI: https://doi.org/10.1007/978-1-4612-3720-4_11
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