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Budd-Chiari Syndrome (How I Treat It) Personal Experience of 250 Cases

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Modern Vascular Surgery

Abstract

Budd-Chiari syndrome (BCS) is a disease of hepatic venous outflow disturbance caused by occlusion of the hepatic veins (HVs) and/or the retrohepatic segment of the inferior vena cava (IVC) proximal to the hepatic venous ostiae. BCS is characterized by clinical manifestation of portal hypertension either with or without IVC hypertension. It was first described by Budd in 1845 and by Chiari in 1899, and it was thought to be a rare disease. Hepatophlebo-vena caval occlusive syndrome might be a better name for this disease entity. Due to a lack of knowledge of the etiology and epidemiology of this disorder, preventative measures are not available. Methods of treatment have been far from uniformly satisfactory. Prognosis is poor if no proper corrective means is instituted. Increasing awareness of this syndrome and rapid development of vascular imaging technology during the last decade have resulted in an increased rate of discovery of this disease in some countries. This paper presents our clinical experience in the management of 250 such patients along with our work on the experimental and epidemiological aspects of this disease and reviews of the related world literature.

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Authors
  1. Zhonggao Wang
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Editors and Affiliations

  1. Long Island Vascular Clinic, Roslyn, NY, 11576, USA

    John B. Chang M.D., F.A.C.S.

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© 1992 Springer-Verlag New York Inc.

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Wang, Z. (1992). Budd-Chiari Syndrome (How I Treat It) Personal Experience of 250 Cases. In: Chang, J.B. (eds) Modern Vascular Surgery. Springer, New York, NY. https://doi.org/10.1007/978-1-4612-2946-9_38

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  • DOI: https://doi.org/10.1007/978-1-4612-2946-9_38

  • Publisher Name: Springer, New York, NY

  • Print ISBN: 978-1-4612-7731-6

  • Online ISBN: 978-1-4612-2946-9

  • eBook Packages: Springer Book Archive

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