Sturge-Weber Disease

  • Concezio Di Rocco
Part of the Principles of Pediatric Neurosurgery book series (PRINCPEDIATR)

Abstract

Neural cutaneous syndromes constitute a rather heterogeneous group from a clinical standpoint. They include several distinct forms that have in common developmental anomalies of neural and other ectodermal structures; in particular, the brain, the skin, and the retina. In many of these syndromes, also known as phakomatoses and ectodermal dysplasias, visceral abnormalities are associated as well.1

Keywords

Retina Lime Neurol Glaucoma Hydrocephalus 

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  • Concezio Di Rocco

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