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Inherited Defects of Muscle Energy Metabolism: Radiologic Evaluation

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Muscle Imaging in Health and Disease

Abstract

Disorders of muscle energy metabolism constitute an extremely diverse group of inherited defects that are generally associated with impaired aerobic and/or anaerobic muscle cell metabolism. These disorders can be categorized as defects of lysosomal glycogen handling, classic glycolysis, lipid metabolism, or mitochondrial structure and/or function.1-4

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Authors
  1. James L. Fleckenstein
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  2. Carl D. Reimers
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  3. Ronald G. Haller
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Editor information

Editors and Affiliations

  1. Department of Radiology, University of Texas Southwestern Medical Center at Dallas, 75235-9071, Dallas, TX, USA

    James L. Fleckenstein MD

  2. RadNet, Inc, 90025-3303, Los Angeles, CA, USA

    John V. Crues III MD

  3. Abteilung für Klinische Neurophysiologie, Universität Göttingen, 37075, Göttingen, Germany

    Carl D. Reimers MD

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© 1996 Springer-Verlag New York, Inc.

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Fleckenstein, J.L., Reimers, C.D., Haller, R.G. (1996). Inherited Defects of Muscle Energy Metabolism: Radiologic Evaluation. In: Fleckenstein, J.L., Crues, J.V., Reimers, C.D. (eds) Muscle Imaging in Health and Disease. Springer, New York, NY. https://doi.org/10.1007/978-1-4612-2314-6_19

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  • DOI: https://doi.org/10.1007/978-1-4612-2314-6_19

  • Publisher Name: Springer, New York, NY

  • Print ISBN: 978-1-4612-7498-8

  • Online ISBN: 978-1-4612-2314-6

  • eBook Packages: Springer Book Archive

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