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Muscle Imaging in Health and Disease pp 193–201Cite as

Spinal Muscular Atrophy

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Abstract

The spinal muscular strophies (SMA) of childhood are inherited neurodegenerative disorders in which there is progressive weakness and wasting of skeletal muscle secondary to degeneration of the anterior horn cells in the spinal cord and brain stem nuclei.1 SMA is the second most common serious neuromuscular disease of childhood, affecting one in 10,000 children.2 SMA of childhood is clinically and genetically a heterogeneous group. Their etiologies are currently unknown, and no specific treatment is available.3

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Authors
  1. Asma Q. Fischer
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  2. Elwood Longenecker
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Editor information

Editors and Affiliations

  1. Department of Radiology, University of Texas Southwestern Medical Center at Dallas, 75235-9071, Dallas, TX, USA

    James L. Fleckenstein MD

  2. RadNet, Inc, 90025-3303, Los Angeles, CA, USA

    John V. Crues III MD

  3. Abteilung für Klinische Neurophysiologie, Universität Göttingen, 37075, Göttingen, Germany

    Carl D. Reimers MD

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© 1996 Springer-Verlag New York, Inc.

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Fischer, A.Q., Longenecker, E. (1996). Spinal Muscular Atrophy. In: Fleckenstein, J.L., Crues, J.V., Reimers, C.D. (eds) Muscle Imaging in Health and Disease. Springer, New York, NY. https://doi.org/10.1007/978-1-4612-2314-6_13

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  • DOI: https://doi.org/10.1007/978-1-4612-2314-6_13

  • Publisher Name: Springer, New York, NY

  • Print ISBN: 978-1-4612-7498-8

  • Online ISBN: 978-1-4612-2314-6

  • eBook Packages: Springer Book Archive

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