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ACTH Resistance Syndromes

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G Proteins, Receptors, and Disease

Part of the book series: Contemporary Endocrinology ((COE,volume 6))

Abstract

The adrenocorticotrophic hormone (ACTH) receptor controls adrenal steroidogene-sis in response to circulating ACTH. The recent cloning of the receptor has opened a new understanding of the normal and pathologic functioning of the adrenal cortex. This chapter will focus on the clinical forms of hereditary ACTH resistance syndromes and their association with abnormalities of the ACTH receptor gene.

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Authors
  1. Constantine Tsigos MD, PHD
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  2. George P. Chrousos MD
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Editor information

Editors and Affiliations

  1. National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bethesda, MD, USA

    Allen M. Spiegel MD (Chief, Metabolic Diseases Branch) (Chief, Metabolic Diseases Branch)

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© 1998 Springer Science+Business Media New York

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Tsigos, C., Chrousos, G.P. (1998). ACTH Resistance Syndromes. In: Spiegel, A.M. (eds) G Proteins, Receptors, and Disease. Contemporary Endocrinology, vol 6. Humana Press, Totowa, NJ. https://doi.org/10.1007/978-1-4612-1802-9_15

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  • DOI: https://doi.org/10.1007/978-1-4612-1802-9_15

  • Publisher Name: Humana Press, Totowa, NJ

  • Print ISBN: 978-1-4612-7290-8

  • Online ISBN: 978-1-4612-1802-9

  • eBook Packages: Springer Book Archive

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