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Congenital Diaphragmatic Hernia

  • Ingo Jester
Chapter

Abstract

Congenital diaphragmatic hernia (CDH) encountered in the neonates is generally diagnosed antenatally and tends to cause significant postnatal management challenges. In this context surgery is only one of the minor challenges. The procedure involves the gentle reposition of the herniated abdominal viscera back into abdomen and repairing the defect either by primary approximation of the defect or by using a patch to separate the abdomen and thoracic cavity. The morbidity in survivals is mainly related to persistence of pulmonary hypertension, gastro-oesophageal reflux with feeding intolerance and recurrence of hernia. The significant mortality associated with CDH is related to severity of pulmonary hypertension, associated cardiac and chromosomal anomalies. The chapter will deal with both open and minimally invasive method of the repair. The management of pulmonary hypertension is outside the scope of this chapter.

Keywords

Congenital diaphragmatic hernia Bochdalek hernia Morgagni hernia Hiatus hernia Thoracoscopy Persistent pulmonary hypertension Pulmonary hypoplasia 

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Copyright information

© Springer-Verlag London Ltd., part of Springer Nature 2018

Authors and Affiliations

  1. 1.Department of Pediatric SurgeryBirmingham Children’s Hospital NHS FTBirminghamUK

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