Abstract
Epithelioid hemangioma is a special type of hemangioma characterized by a benign although locally aggressive behavior, composed by proliferated small-caliber blood vessels lined by plump endothelial cells with an epithelioid morphology. It is rare in bone, where it grows in a more solid fashion than its soft tissue counterpart. It is seen more often between 20 and 60 years of age. Long bones of the extremities are preferably affected and may be multifocal. EH is usually painful. Regional lymph node metastases and soft tissue extension of the tumor do not mean altered aggressiveness. Besides endothelial markers, epithelial markers are positive. It has a 10 % recurrence risk.
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Kalil, R.K. (2015). Epithelioid Hemangioma. In: Santini-Araujo, E., Kalil, R., Bertoni, F., Park, YK. (eds) Tumors and Tumor-Like Lesions of Bone. Springer, London. https://doi.org/10.1007/978-1-4471-6578-1_33
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DOI: https://doi.org/10.1007/978-1-4471-6578-1_33
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