Abstract
Multiple enchondromatosis (Ollier’s disease) is a rare, nonhereditary developmental abnormality involving defective endochondral ossification. It is characterized by multiple intraosseous and subperiosteal cartilaginous tumors, ranging in size from microscopic foci to bulky masses. The skeleton is most frequently affected unilaterally, but bilateral involvement is also observed. The association of enchondromatosis with multiple hemangiomas of soft tissue was reported in 1881 by Maffucci (18 years before Ollier), and this clinical presentation is generally referred to as “Maffucci’s syndrome.”
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Park, YK. (2015). Multiple Enchondromatosis (Ollier’s Disease). In: Santini-Araujo, E., Kalil, R., Bertoni, F., Park, YK. (eds) Tumors and Tumor-Like Lesions of Bone. Springer, London. https://doi.org/10.1007/978-1-4471-6578-1_17
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DOI: https://doi.org/10.1007/978-1-4471-6578-1_17
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