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Chorea pp 211–219Cite as

Chorea in Inherited Ataxias

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Abstract

Inherited ataxias (IAs) can present with non-cerebellar signs and symptoms, especially those with movement disorders. This chapter will provide a review analyzing the presence of chorea in patients with inherited ataxias (IAs). Chorea can be found among different types of IA: autosomal recessive cerebellar ataxias (ARCAs), such as ataxia telangiectasia (more commonly), and Friedreich ataxia (more rarely). In the group of spinocerebellar ataxias (SCAs), chorea can be found more commonly in patients with SCA type 17, and in dentatorubral-pallidoluysian atrophy (DRPLA).

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Author information

Authors and Affiliations

  1. Movement Disorders Unit, Neurology Service, Internal Medicine Department, Hospital de Clínicas, Federal University of Paraná, Rua General Carneiro 1103/102, Centro, 80060-150, Curitiba, PR, Brazil

    Hélio A. Ghizoni Teive & Renato Puppi Munhoz

  2. Department of Neurology, University of Toronto, Toronto, ON, Canada

    Renato Puppi Munhoz

Authors
  1. Hélio A. Ghizoni Teive
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  2. Renato Puppi Munhoz
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Corresponding author

Correspondence to Hélio A. Ghizoni Teive .

Editor information

Editors and Affiliations

  1. Parkinson Disease and Movement Disorders Program and Neurology Department, Hospital de Clínicas, José de San Martín, Buenos Aires, Argentina

    Federico E. Micheli

  2. Parkinson's Disease and Movement Disorders Program, Henry Ford West Bloomfield Hospital, West Bloomfield, Michigan, USA

    Peter A. LeWitt

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© 2014 Springer-Verlag London

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Teive, H.A.G., Munhoz, R.P. (2014). Chorea in Inherited Ataxias. In: Micheli, F., LeWitt, P. (eds) Chorea. Springer, London. https://doi.org/10.1007/978-1-4471-6455-5_12

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  • DOI: https://doi.org/10.1007/978-1-4471-6455-5_12

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  • Publisher Name: Springer, London

  • Print ISBN: 978-1-4471-6454-8

  • Online ISBN: 978-1-4471-6455-5

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