Abstract
A double-inlet left ventricle (DILV) or single ventricle is a congenital heart defect (CHD) occurring in 5 in 100,000 newborns that both the left atrium (LA) and the right atrium (RA) feed into the LV; indeed, 2 separated atrioventricular ostia open in a morphological LV. The right ventricle (RV) is hypoplastic or sometimes does not exist [1–3].
This is a preview of subscription content, log in via an institution to check access.
Access this chapter
Tax calculation will be finalised at checkout
Purchases are for personal use only
References
Dhanantwari P, Lee E, Krishnan A, et al. Human cardiac development in the first trimester: a high-resolution magnetic resonance imaging and episcopic fluorescence image capture atlas. Circulation. 2009;120(4):343–51.
Sizarov A, Ya J, de Boer BA, et al. Formation of the building plan of the human heart: morphogenesis, growth, and differentiation. Circulation. 2011;123(10):1125–35.
Koshiba-Takeuchi K, Mori AD, et al. Reptilian heart development and the molecular basis of cardiac chamber evolution. Nature. 2009;461(7260):95–8.
Warnes CA. Congenital heart disease for the adult cardiologist. Transposition of the great arteries. Circulation. 2006;114:2699–709.
Warnes CA, Williams RG, Bashore TM, et al. American Heart Association. ACC/AHA 2008 Guidelines for the Management of Adults with Congenital Heart Disease. Circulation. 2008;118:e714–e833.
Bruneau BG, Logan M, Davis N, et al. Chamber-specific cardiac expression of Tbx5 and heart defects in Holt-Oram syndrome. Dev Biol. 1999;211(1):100–8.
Takeuchi JK, Ohgi M, Koshiba-Takeuchi K, et al. Tbx5 specifies the left/right ventricles and ventricular septum position during cardiogenesis. Development. 2003;130(24):5953–64.
Chin AJ, Whitehead KK, Watrous RL. Insights after 40 years of the Fontan Operation. World J Pediatr Congenit Heart Surg. 2010;1:328–43.
DeLeval MR, Deanfield JE. Four decades of Fontan Palliation. Nat Rev Cardiol. 2010;7:520–7.
Author information
Authors and Affiliations
Corresponding author
Editor information
Editors and Affiliations
Electronic Supplementary Material
Below is the link to the electronic supplementary material.
Transthoracic echocardiography in 4 chamber view showing main ventricle with LV morphology (DILV), receiving two separate atrioventricular valves (WMV 356 kb)
Transthoracic echocardiography in parasternal long axis view showing DILV and transposition of great arteries (WMV 325 kb)
Trans esophageal echocardiography in transgasteric short axis and long axis view showing main ventricle with LV morphology (DILV) and Aorta arises from the rudimentary anterior chamber (MPG 1200 kb)
Trans esophageal echocardiography in transgasteric short axis and long axis view showing main ventricle with LV morphology (DILV) and Aorta arises from the rudimentary anterior chamber (MPG 1258 kb)
Trans esophageal echocardiography in long axis view demonstrating transposition of great arteries and severe pulmonary stenosis (MPG 1108 kb)
Rights and permissions
Copyright information
© 2014 Springer-Verlag London
About this chapter
Cite this chapter
Sadeghpour, A., Alizadehasl, A. (2014). Double-Inlet Ventricular and Univentricular Heart. In: Sadeghpour, A., Kyavar, M., Alizadehasl, A. (eds) Comprehensive Approach to Adult Congenital Heart Disease. Springer, London. https://doi.org/10.1007/978-1-4471-6383-1_30
Download citation
DOI: https://doi.org/10.1007/978-1-4471-6383-1_30
Published:
Publisher Name: Springer, London
Print ISBN: 978-1-4471-6382-4
Online ISBN: 978-1-4471-6383-1
eBook Packages: MedicineMedicine (R0)