Abstract
Obviously, the proper management of every disease needs the proper definition and classification. Pulmonary hypertension (PH) which is a hemodynamic and pathophysiological condition has been defined as raised mean pulmonary arterial pressure ≥25 mmHg at rest that is confirmed by right heart catheterization (RHC). PH has been found in multiple different clinical conditions, and the American and European guidelines have been provided a clear classification based on the pathophysiological mechanisms, clinical presentations, and therapeutic approaches (Table 15.1).
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Sadeghpour, A., Alizadehasl, A. (2014). Pulmonary Hypertension Associated with Congenital Heart Disease, Eisenmenger Syndrome. In: Sadeghpour, A., Kyavar, M., Alizadehasl, A. (eds) Comprehensive Approach to Adult Congenital Heart Disease. Springer, London. https://doi.org/10.1007/978-1-4471-6383-1_15
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DOI: https://doi.org/10.1007/978-1-4471-6383-1_15
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