Abstract
Arrhythmogenic right ventricular dysplasia (ARVD) is a nonischemic, genetically determined, myocardial disease that involves primarily the right ventricle (RV) and is associated with life-threatening ventricular arrhythmias. Its prevalence has been estimated to vary from 1:2,500 to 1:5,000 and it is seen predominantly in males [1]. About 30–50 % of cases have a familial distribution [1]. ARVD is a major cause of sudden cardiac death in young athletes. Symptoms are usually exercise-related.
This is a preview of subscription content, log in via an institution to check access.
Access this chapter
Tax calculation will be finalised at checkout
Purchases are for personal use only
References
Peters S, Trummel M, Meyners W. Prevalence of right ventricular dysplasia-cardiomyopathy in a non-referral hospital. Int J Cardiol. 2004;97:499–501. doi:10.1016/j.ijcard.2003.10.037.
Marcus FI, McKenna WJ, Sherrill D, Basso C, Bauce B, Bluemke DA, et al. Diagnosis of arrhythmogenic right ventricular cardiomyopathy/dysplasia: proposed modification of the task force criteria. Circulation. 2010;121:1533–41. doi:10.1161/CIRCULATIONAHA.108.840827.
Kimura F, Matsuo Y, Nakajima T, Nishikawa T, Kawamura S, Sannohe S, et al. Myocardial fat at cardiac imaging: how can we differentiate pathologic from physiologic fatty infiltration? Radiographics. 2010;30:1587–602. doi:10.1148/rg.306105519.
Adriaensen ME, Schaefer-Prokop CM, Duyndam DA, Zonnenberg BA, Prokop M. Fatty foci in the myocardium in patients with tuberous sclerosis complex: common finding at CT. Radiology. 2009;253:359–63. doi:10.1148/radiol.2533082118.
Hunter S. The heart in muscular dystrophy. Br Med Bull. 1980;36:133–4.
Kim E, Choe YH, Han BK, Kim SM, Kim JS, Park SW, et al. Right ventricular fat infiltration in asymptomatic subjects: observations from ECG-gated 16-slice multidetector CT. J Comput Assist Tomogr. 2007;31:22–8.
Kirsch J, Williamson EE, Glockner JF. Focal macroscopic fat deposition within the right ventricular wall in asymptomatic patients undergoing screening EBCT coronary calcium scoring examinations. Int J Cardiovasc Imaging. 2008;24:223–7. doi:10.1007/s10554-007-9232-x.
Zafar HM, Litt HI, Torigian DA. CT imaging features and frequency of left ventricular myocardial fat in patients with CT findings of chronic left ventricular myocardial infarction. Clin Radiol. 2008;63:256–62. doi:10.1016/j.crad.2007.08.007.
Ahn SS, Kim YJ, Hur J, Lee HJ, Kim TH, Choe KO, et al. CT detection of subendocardial fat in myocardial infarction. AJR Am J Roentgenol. 2009;192:532–7. doi:10.2214/AJR.08.1608.
Ichikawa Y, Kitagawa K, Chino S, Ishida M, Matsuoka K, Tanigawa T, et al. Adipose tissue detected by multislice computed tomography in patients after myocardial infarction. JACC Cardiovasc Imaging. 2009;2:548–55. doi:10.1016/j.jcmg.2009.01.010.
Heyer CM, Kagel T, Lemburg SP, Bauer TT, Nicolas V. Lipomatous hypertrophy of the interatrial septum: a prospective study of incidence, imaging findings, and clinical symptoms. Chest. 2003;124:2068–73.
Stojanovska J, Attili AK. AJR teaching file: fat-containing mass in the interatrial septum. AJR Am J Roentgenol. 2010;195:S73–5. doi:10.2214/AJR.09.7173.
Salanitri JC, Pereles FS. Cardiac lipoma and lipomatous hypertrophy of the interatrial septum: cardiac magnetic resonance imaging findings. J Comput Assist Tomogr. 2004;28:852–6.
Author information
Authors and Affiliations
Rights and permissions
Copyright information
© 2013 Springer-Verlag London
About this chapter
Cite this chapter
Mazur, W., Siegel, M.J., Miszalski-Jamka, T., Pelberg, R. (2013). Arrhythmogenic Right Ventricular Dysplasia. In: CT Atlas of Adult Congenital Heart Disease. Springer, London. https://doi.org/10.1007/978-1-4471-5088-6_7
Download citation
DOI: https://doi.org/10.1007/978-1-4471-5088-6_7
Published:
Publisher Name: Springer, London
Print ISBN: 978-1-4471-5087-9
Online ISBN: 978-1-4471-5088-6
eBook Packages: MedicineMedicine (R0)