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Atrioventricular Valve Abnormalities

  • Wojciech Mazur
  • Marilyn J. Siegel
  • Tomasz Miszalski-Jamka
  • Robert Pelberg
Chapter

Abstract

Ebstein anomaly is a myopathy of the right ventricle that results in variable degrees of failure of delamination of the valve leaflets, leading to tricuspid valve regurgitation and right ventricular dysfunction. The classic pathology is apical (downward) displacement of the tricuspid valve leaflets (most frequently septal followed by posterior and anterior leaflets) with abnormal adherence of the leaflets to the underlying myocardium.

Keywords

Mitral Valve Mitral Regurgitation Tricuspid Valve Mitral Stenosis Mitral Valve Prolapse 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

References

  1. 1.
    Edwards WD. Embryology and pathologic features of Ebstein’s anomaly. Prog Pediatr Cardiol. 1993;2:5–15.CrossRefGoogle Scholar
  2. 2.
    Carpentier A, Chauvaud S, Mace L, Relland J, Mihaileanu S, Marino JP, et al. A new reconstructive operation for Ebstein’s anomaly of the tricuspid valve. J Thorac Cardiovasc Surg. 1988;96:92–101.PubMedGoogle Scholar
  3. 3.
    Lincoln T, Stewart C, Shah P. An unusual first presentation of Ebstein’s anomaly in a 72-year-old patient. Ann Thorac Surg. 2012;93:e19–20. doi: 10.1016/j.athoracsur.2011.08.024.PubMedCrossRefGoogle Scholar
  4. 4.
    Abbara S, Soni AV, Cury RC. Evaluation of cardiac function and valves by multidetector row computed tomography. Semin Roentgenol. 2008;43:145–53. doi: 10.1053/j.ro.2008.01.009.PubMedCrossRefGoogle Scholar
  5. 5.
    Goo HW, Park IS, Ko JK, Kim YH, Seo DM, Yun TJ, et al. CT of congenital heart disease: normal anatomy and typical pathologic conditions. Radiographics. 2003;23 Spec No:S147–65. doi: 10.1148/rg.23si035501.PubMedCrossRefGoogle Scholar
  6. 6.
    Hughes Jr D, Siegel MJ. Computed tomography of adult congenital heart disease. Radiol Clin North Am. 2010;48:817–35. doi: 10.1016/j.rcl.2010.04.005.PubMedCrossRefGoogle Scholar
  7. 7.
    Tandon R, Edwards JE. Tricuspid atresia. A re-evaluation and classification. J Thorac Cardiovasc Surg. 1974;67:530–42.PubMedGoogle Scholar
  8. 8.
    Weinberg PM. Anatomy of tricuspid atresia and its relevance to current forms of surgical therapy. Ann Thorac Surg. 1980;29:306–11.PubMedCrossRefGoogle Scholar
  9. 9.
    Mochizuki T, Ohtani T, Higashino H, Sugawara Y, Tsuda T, Sekiya M, et al. Tricuspid atresia with atrial septal defect, ventricular ­septal defect, and right ventricular hypoplasia demonstrated by multidetector computed tomography. Circulation. 2000;102:E164–5.PubMedCrossRefGoogle Scholar
  10. 10.
    Siegel MJ. CT evaluation of congenital heart disease in adults. Appl Radiol. 2005;34:61–8.Google Scholar
  11. 11.
    Siegel MJ, Bhalla S, Gutierrez FR, Billadello JB. MDCT of postoperative anatomy and complications in adults with cyanotic heart disease. AJR Am J Roentgenol. 2005;184:241–7.PubMedCrossRefGoogle Scholar
  12. 12.
    Niwayama G. Cor triatriatum. Am Heart J. 1960;59:291–317.PubMedCrossRefGoogle Scholar
  13. 13.
    Van Praagh R, Corsini I. Cor triatriatum: pathologic anatomy and a consideration of morphogenesis based on 13 postmortem cases and a study of normal development of the pulmonary vein and atrial septum in 83 human embryos. Am Heart J. 1969;78:379–405.PubMedCrossRefGoogle Scholar
  14. 14.
    Ucar O, Vural M, Cicekcioglu H, Pasaoglu L, Aydogdu S, Koparal S. Case report: multidetector CT presentation of a parachute-like asymmetric mitral valve. Br J Radiol. 2008;81:e266–8. doi: 10.1259/bjr/20218809.PubMedCrossRefGoogle Scholar
  15. 15.
    Ruckman RN, Van Praagh R. Anatomic types of congenital mitral stenosis: report of 49 autopsy cases with consideration of diagnosis and surgical implications. Am J Cardiol. 1978;42:592–601.PubMedCrossRefGoogle Scholar
  16. 16.
    Bano-Rodrigo A, Van Praagh S, Trowitzsch E, Van Praagh R. Double-orifice mitral valve: a study of 27 postmortem cases with developmental, diagnostic and surgical considerations. Am J Cardiol. 1988;61:152–60.PubMedCrossRefGoogle Scholar
  17. 17.
    Zalzstein E, Hamilton R, Zucker N, Levitas A, Gross GJ. Presentation, natural history, and outcome in children and adolescents with double orifice mitral valve. Am J Cardiol. 2004;93:1067–9. doi: 10.1016/j.amjcard.2004.01.015.PubMedCrossRefGoogle Scholar
  18. 18.
    Collins 2nd RT, Ryan M, Gleason MM. Images in cardiovascular medicine. Mitral arcade: a rare cause of fatigue in an 18-year-old female. Circulation. 2010;121:e379–83. doi: 10.1161/CIR.0b013e3181db1ee4.PubMedCrossRefGoogle Scholar
  19. 19.
    Morris MF, Williamson EE, Topilsky Y, Espinosa RE, Cetta F, Burkhart HM, et al. Multi-imaging assessment of the congenital mitral arcade. J Am Coll Cardiol. 2011;57(18):1856. doi: 10.1016/j.jacc.2010.06.069.PubMedCrossRefGoogle Scholar
  20. 20.
    Feuchtner GM, Alkadhi H, Karlo C, Sarwar A, Meier A, Dichtl W, et al. Cardiac CT angiography for the diagnosis of mitral valve prolapse: comparison with echocardiography1. Radiology. 2010;254:374–83. doi: 10.1148/radiol.2541090393.PubMedCrossRefGoogle Scholar
  21. 21.
    Di Segni E, Kaplinsky E, Klein HO. Color Doppler echocardiography of isolated cleft mitral valve. Roles of the cleft and the accessory chordae. Chest. 1992;101:12–5.PubMedCrossRefGoogle Scholar
  22. 22.
    McDonald RW, Ott GY, Pantely GA. Cleft in the anterior and posterior leaflet of the mitral valve: a rare anomaly. J Am Soc Echocardiogr. 1994;7:422–4.PubMedGoogle Scholar
  23. 23.
    Kohl T, Silverman NH. Comparison of cleft and papillary muscle position in cleft mitral valve and atrioventricular septal defect. Am J Cardiol. 1996;77:164–9.PubMedCrossRefGoogle Scholar
  24. 24.
    Chen JJ, Manning MA, Frazier AA, Jeudy J, White CS. CT angiography of the cardiac valves: normal, diseased, and postoperative appearances. Radiographics. 2009;29:1393–412. doi: 10.1148/rg.295095002.PubMedCrossRefGoogle Scholar
  25. 25.
    Morris MF, Maleszewski JJ, Suri RM, Burkhart HM, Foley TA, Bonnichsen CR, et al. CT and MR imaging of the mitral valve: radiologic-pathologic correlation. Radiographics. 2010;30:1603–20. doi: 10.1148/rg.306105518.PubMedCrossRefGoogle Scholar

Copyright information

© Springer-Verlag London 2013

Authors and Affiliations

  • Wojciech Mazur
    • 1
  • Marilyn J. Siegel
    • 2
  • Tomasz Miszalski-Jamka
    • 3
    • 4
  • Robert Pelberg
    • 1
  1. 1.The Christ Hospital Heart and Vascular Center of Greater CincinnatiThe Lindner Center for Research and EducationCincinnatiUSA
  2. 2.Mallinckrodt Institute of RadiologyWashington University School of MedicineSt. LouisUSA
  3. 3.Department of Clinical Radiology and Imaging Diagnostics4th Military HospitalWrocławPoland
  4. 4.Center for Diagnosis Prevention and TelemedicineJohn Paul II HospitalKrakówPoland

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