Abstract
Ebstein anomaly is a myopathy of the right ventricle that results in variable degrees of failure of delamination of the valve leaflets, leading to tricuspid valve regurgitation and right ventricular dysfunction. The classic pathology is apical (downward) displacement of the tricuspid valve leaflets (most frequently septal followed by posterior and anterior leaflets) with abnormal adherence of the leaflets to the underlying myocardium.
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Mazur, W., Siegel, M.J., Miszalski-Jamka, T., Pelberg, R. (2013). Atrioventricular Valve Abnormalities. In: CT Atlas of Adult Congenital Heart Disease. Springer, London. https://doi.org/10.1007/978-1-4471-5088-6_12
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