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Prune Belly Syndrome

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Rickham's Neonatal Surgery

Abstract

Prune Belly Syndrome (PBS) is a rare anomaly of the anterior abdominal wall, urinary tract and undescended testes. It is thought to be caused by transient obstruction of the urethra between 10 and 20 weeks of gestation, leading to massive dilatation of the bladder which resolves in the third trimester. The atrophic abdominal wall and cryptorchidism are secondary to the enlarged bladder. Management primarily requires treatment of the intraabdominal testes.

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Author information

Authors and Affiliations

  1. University of Melbourne & Royal Children’s Hospital, Parkville, VIC, Australia

    John M. Hutson BS, MD(Monash), MD, DSc(Melb)

Authors
  1. John M. Hutson BS, MD(Monash), MD, DSc(Melb)
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Correspondence to John M. Hutson BS, MD(Monash), MD, DSc(Melb) .

Editor information

Editors and Affiliations

  1. Division of Child Health, Alder Hey Children’s NHS Foundation Trust, Liverpool, United Kingdom

    Paul D. Losty

  2. University of Pennsylvania , Philadelphia, Pennsylvania, USA

    Alan W. Flake

  3. Childrens Hospital, University of Helsinki, Helsinki, Finland

    Risto J. Rintala

  4. Royal Children’s Hospital, University of Melbourne, Parkville, Victoria, Australia

    John M. Hutson

  5. Department of Surgery, Meiji University of Integrative Medicine, Kyoto, Japan

    Naomi lwai

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Hutson, J.M. (2018). Prune Belly Syndrome. In: Losty, P., Flake, A., Rintala, R., Hutson, J., lwai, N. (eds) Rickham's Neonatal Surgery. Springer, London. https://doi.org/10.1007/978-1-4471-4721-3_67

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  • DOI: https://doi.org/10.1007/978-1-4471-4721-3_67

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  • Publisher Name: Springer, London

  • Print ISBN: 978-1-4471-4720-6

  • Online ISBN: 978-1-4471-4721-3

  • eBook Packages: MedicineMedicine (R0)

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