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Aortic Anomalies

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Magnetic Resonance Imaging of Congenital Heart Disease

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Abstract

Aortic congenital anomalies are common and comprised of a heterogenous group of conditions that may be due to either embryological or vessel wall architectural defects. Imaging is crucial for diagnosis, management, follow-up and reassessment after intervention of these conditions. Cardiovascular magnetic resonance (CMR) is a valuable non-invasive imaging method for providing detailed anatomical, functional and haemodynamic information on a wide spectrum of aortic anomalies and intra- and extracardiac associated abnormalities. The technique is radiation free and is ideally suited for diagnoses as well as serial follow-up pre and post interventions such as a dilated aortic root in Marfan syndrome and aortic coarctation. This chapter reviews the role of CMR in the management of a wide spectrum of congenital aortic anomalies and provides CMR scanning protocols and clinical reporting of the anomalies both in the native and post-repair states.

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Author information

Authors and Affiliations

  1. Cardiovascular Magnetic Resonance Unit, The Royal Brompton Hospital, Sydney Street, London, SW3 6NP, UK

    Sylvia S. M. Chen MBBS, M.D., FRACP

  2. Cardiovascular Magnetic Resonance Unit, Royal Brompton Hospital and National Heart and Lung Institute, Imperial College London, Sydney Street, London, SW3 6NP, UK

    Raad H. Mohiaddin M.D., Ph.D., FRCR, PRCP, FESC

Authors
  1. Sylvia S. M. Chen MBBS, M.D., FRACP
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  2. Raad H. Mohiaddin M.D., Ph.D., FRCR, PRCP, FESC
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Corresponding author

Correspondence to Sylvia S. M. Chen MBBS, M.D., FRACP .

Editor information

Editors and Affiliations

  1. , Stritch School of Medicine, Loyola University Chicago, S. First Ave. 2160, Maywood, 60153, Illinois, USA

    Mushabbar A. Syed

  2. Magnetic Resonance Unit, Royal Brompton Hospital, Sydney Street, London, SW3 6NP, United Kingdom

    Raad H. Mohiaddin

12.1 Electronic Supplementary Material

Below is the link to the electronic supplementary material.

Multi-intensity projection (MIP) reconstruction of MRA after contrast enhancement in severe native coarctation of the aorta with collaterals (AVI 10795 KB)

Aneurysm at the site of previous coarctation repair. There is persistent flow into the aneurysm despite previous stent implantation (AVI 11544 KB)

Surface rendered 3D reconstruction after contrast enhanced MRA of truncus arteriosus type 1 with a short main pulmonary after arising from the common arterial trunk (AVI 15676 KB)

Surface rendered 3D reconstruction after contrast enhanced MRA showing a diverticulum of Kommerell at the origin of an anomalous left subclavian artery from a right aortic arch (AVI 11662 KB)

Surface rendered 3D reconstruction after contrast enhanced MRA of a double aortic arch (AVI 11528 KB)

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© 2012 Springer-Verlag London

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Chen, S.S.M., Mohiaddin, R.H. (2012). Aortic Anomalies. In: Syed, M., Mohiaddin, R. (eds) Magnetic Resonance Imaging of Congenital Heart Disease. Springer, London. https://doi.org/10.1007/978-1-4471-4267-6_12

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  • DOI: https://doi.org/10.1007/978-1-4471-4267-6_12

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  • Publisher Name: Springer, London

  • Print ISBN: 978-1-4471-4266-9

  • Online ISBN: 978-1-4471-4267-6

  • eBook Packages: MedicineMedicine (R0)

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