Abstract
A 6-month-old girl presented in cardiac failure and was found to have a large, poorly contractile left ventricle. A convincing appearance of a normal left coronary artery was subsequently found to be misleading, with the artery in fact arising from the main pulmonary artery. Left ventricular damage was severe at presentation and despite immediate surgery the child ultimately succumbed. Anomalous left coronary artery from the pulmonary artery, previously referred to as Bland-White-Garland syndrome, is a rare condition, easily missed if fastidious attention is not given to identifying the origin of the left coronary artery and direction of blood flow within it. Prompt recognition and surgery offer the best chance of a successful outcome.
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© 2016 Springer-Verlag London
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Spentzou, G., Smith, B.G. (2016). Coronary Artery Imaging Is Crucial. In: Magee, A., Till, J., Seale, A. (eds) Practical Pediatric Cardiology. Springer, London. https://doi.org/10.1007/978-1-4471-4183-9_7
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DOI: https://doi.org/10.1007/978-1-4471-4183-9_7
Publisher Name: Springer, London
Print ISBN: 978-1-4471-4182-2
Online ISBN: 978-1-4471-4183-9
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