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Hypermobility of Joints pp 125–149Cite as

Ehlers—Danlos Syndrome

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Abstract

The Ehlers—Danlos syndrome (EDS) is an inherited disorder of connective tissue which is characterised by the clinical triad of articular hypermobility, dermal extensibility and cutaneous scarring. The manifestations are very variable although usually fairly consistent within any kindred, and it has become increasingly evident that EDS is very heterogeneous.

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Author information

Authors and Affiliations

  1. MRC Research Unit for Inherited Skeletal Disorders, Medical School and Groot Schuur Hospital, University of Cape Town, South Africa

    Peter Beighton MD, PhD, FRCP, DCH (Professor of Human Genetics and Director)

  2. Guy’s Hospital, London, SE1 9RT, England

    Rodney Grahame MD, FRCP (Consultant Rheumatologist)

  3. University of Leeds, Harrogate, England

    Howard Bird MD, MRCP (Lecturer in Rheumatology, Consultant Rheumatologist)

  4. General Infirmary at Leeds and Royal Bath Hospital, Harrogate, England

    Howard Bird MD, MRCP (Lecturer in Rheumatology, Consultant Rheumatologist)

Authors
  1. Peter Beighton MD, PhD, FRCP, DCH
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  2. Rodney Grahame MD, FRCP
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  3. Howard Bird MD, MRCP
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© 1983 Springer-Verlag Berlin Heidelberg

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Beighton, P., Grahame, R., Bird, H. (1983). Ehlers—Danlos Syndrome. In: Hypermobility of Joints. Springer, London. https://doi.org/10.1007/978-1-4471-3510-4_9

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  • DOI: https://doi.org/10.1007/978-1-4471-3510-4_9

  • Publisher Name: Springer, London

  • Print ISBN: 978-1-4471-3512-8

  • Online ISBN: 978-1-4471-3510-4

  • eBook Packages: Springer Book Archive

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