Pulmonary Atresia and Intact Ventricular Septum

  • R. M. Freedom
  • P. E. Burrows
  • J. F. Smallhorn

Abstract

The drama and success that so characterizes the patient with complete transposition of the great arteries has thus far eluded the patient with pulmonary atresia and intact ventricular septum [48, 89] (Fig. 19.1). Despite the somewhat simplistic designation “pulmonary atresia and intact ventricular septum”, this is a very complex disorder with a wide anatomical and clinical spectrum. The desirability of defining two groups of patients with this disorder, those with small right ventricles and those with large right ventricles, is today inadequate [27, 33]. For many patients afflicted with this disorder, it is the potential for the peculiar involvement of the coronary artery circulation that sets the stage for disappointment and frustration [10, 18, 22, 34, 48, 50, 57, 61, 62, 74, 84, 95, 96, 109, 121, 127, 130, 132]. Pulmonary atresia and intact ventricular septum is a global disorder of the right ventricle, and the myocardium may be terribly disadvantaged.

Keywords

Catheter Ischemia Attenuation Prostaglandin Mane 

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Copyright information

© Springer-Verlag London Limited 1992

Authors and Affiliations

  • R. M. Freedom
  • P. E. Burrows
  • J. F. Smallhorn

There are no affiliations available

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