Abstract
The hereditary system disorders of the nervous system form a large group of diseases in which the characteristic feature is degeneration of one or more systems of neurons, and of their interconnecting projections. In some the pathogenesis is relatively well understood, for example subacute combined degeneration of the spinal cord, but in others, for example motor neuron disease, the cause is obscure. The term ‘system degeneration’, which is often used to describe these degenerative disorders, indicates that certain functional groups of neurons and their axons are selectively affected, resulting in clearly recognisable patterns of abnormality.
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© 1983 Springer-Verlag Berlin Heidelberg
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Weller, R.O., Swash, M., McLellan, D.L., Scholtz, C.L. (1983). Hereditary and System Disorders of the Nervous System. In: Clinical Neuropathology. Springer, London. https://doi.org/10.1007/978-1-4471-1335-5_14
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DOI: https://doi.org/10.1007/978-1-4471-1335-5_14
Publisher Name: Springer, London
Print ISBN: 978-1-4471-1337-9
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