Diaphyseal Dysplasia (Camurati-Engelmann Disease)
Camurati (1922) described a seven-year-old boy with painful lower limbs and diaphyseal cortical thickening in the long bones of the legs. The 55-year-old father and eight of their family members in four generations were thought to be affected, and the condition was termed ‘hereditary symmetrical osteitis’.
KeywordsPainful Lower Limb Radiographic Manifestation Cortical Hyperostosis Proximal Femoral Shaft Optic Nerve Decompression
Unable to display preview. Download preview PDF.
- Allen DT, Saunders AM, Northway WH JR, Williams GF, Schafer IA (1970) Corticosteroids in the treatment of Engelmann’s disease: Progressive diaphyseal dysplasia. Pediatries 46: 523Google Scholar
- Camurati M (1922) Di un raro caso di osteite simmetrica ereditaria degli arti inferiori. Chir Organi Mov 6: 662Google Scholar
- Clawson DK, Loop JW (1964) Progressive diaphyseal dysplasia (Engelmann’s disease). J Bone Joint Surg [Am] 46: 143Google Scholar
- Engelmann G (1929) Ein Fall von Osteopathia Hyperostica (sclerotisans) Multiplex Infantalis. Fortschr Roentgenstr 39: 1101Google Scholar
- Girdany BR, Sane S, Graham CB (1973) Engelmann’s disease. In: Kaufmann HJ (ed) Intrinsic diseases of bones. Basel, Karger (Progress in pediatric radiology, vol 4, p 414 )Google Scholar
- Griffiths DL (1956) Engelmann’s disease. J Bone Joint Surg 38: 312Google Scholar
- Hundley JD, Wilson FC (1973) Progressive diaphyseal dysplasia. J Bone Joint Surg [Am] 55: 461Google Scholar
- Ribbing S (1949) Hereditary multiple diaphyseal sclerosis. Acta Radiol (Stockh) 31: 522Google Scholar