Abstract
Disorders of sex development (DSD) are “congenital conditions in which development of chromosomal, gonadal, or anatomic sex is atypical” [1]. The conditions subsumed under this superordinate term are individually rare but, in the aggregate, have an estimated incidence of 0.5–1% [2]. Clinical management of DSD (formerly referred to as “intersex”) had stood largely unchallenged from the mid-1950s until the early 1990s. At that time, criticism of various aspects of clinical practice in DSD emerged from several perspectives [3], perhaps most notably from affected adults who expressed dissatisfaction with their treatment [4, 5]. A confluence of advances in the diagnosis of DSD and appraisal of surgical and psychological outcomes has led to a reexamination of assumptions and clinical practice.
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Asciutto, A.J., Haddad, E., Green, J., Sandberg, D.E. (2011). Patient-Centered Care: Caring for Families Affected by Disorders of Sex Development. In: New, M., Simpson, J. (eds) Hormonal and Genetic Basis of Sexual Differentiation Disorders and Hot Topics in Endocrinology: Proceedings of the 2nd World Conference. Advances in Experimental Medicine and Biology, vol 707. Springer, New York, NY. https://doi.org/10.1007/978-1-4419-8002-1_30
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