Abstract
Noonan syndrome is associated with valvular pulmonary stenosis, Williams syndrome is associated with supravalvular pulmonary (and aortic) stenosis, while Allagile and congenital Rubella are associated with peripheral pulmonary stenosis. Pulmonary stenosis, even when severe is typically asymptomatic. Right heart failure develops in critical or long-standing pulmonary stenosis. Valvular pulmonary stenosis is almost always associated with systolic click preceding the systolic ejection murmur. Soft P2 may indicate abnormal pulmonary valve due to pulmonary stenosis. Mild pulmonary stenosis rarely worsens in intensity. SBE prophylaxis is not required in pulmonary stenosis, regardless of severity.
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© 2011 Springer Science+Business Media, LLC
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Hoffman, J.F., Mehrotra, S.M., Buckvold, S.M. (2011). Pulmonary Stenosis. In: Abdulla, Ri. (eds) Heart Diseases in Children. Springer, Boston, MA. https://doi.org/10.1007/978-1-4419-7994-0_10
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DOI: https://doi.org/10.1007/978-1-4419-7994-0_10
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