Abstract
Pulmonary arterial hypertension (PAH) can be idiopathic or associated with other disease processes. Systemic sclerosis is an example of one disease that is associated with the development of PAH. Regardless of the cause, PAH can have an insidious onset and is often difficult to diagnose because of the subtle associated signs and symptoms as well as the lack of a definitive noninvasive diagnostic test.
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Swift, I., Weaver, S., D’Alonzo, G. (2012). Pulmonary Hypertension. In: Mahmoudi, M. (eds) Challenging Cases in Pulmonology. Springer, New York, NY. https://doi.org/10.1007/978-1-4419-7098-5_11
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DOI: https://doi.org/10.1007/978-1-4419-7098-5_11
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