Muir-Torre Syndrome

  • Pedro Mercader
Part of the Advances in Experimental Medicine and Biology book series (AEMB, volume 685)


Muir-Torre syndrome (MTS) is an autosomal dominant genodermatosis that consists of unusual cutaneous sebaceous neoplasm, with or without kerathoacantomas and one or more low-grade visceral malignancies, with or without colonic polyps, in the absence of other predisposing factors. This chapter presents a review of the principal clinical and genetic findings in this syndrome and discusses its relation with Lynch sy


Lynch Syndrome Sebaceous Gland Hereditary Nonpolyposis Colorectal Cancer Germinative Cell Sebaceous Carcinoma 
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Copyright information

© Landes Bioscience and Springer Science+Business Media 2010

Authors and Affiliations

  • Pedro Mercader
    • 1
  1. 1.Dermatology Service Hospital GeneralUniversitario Morales MeseguerMurciaSpain

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