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Diseases of DNA Repair pp 186–195Cite as

Muir-Torre Syndrome

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Part of the book series: Advances in Experimental Medicine and Biology ((AEMB,volume 685))

Abstract

Muir-Torre syndrome (MTS) is an autosomal dominant genodermatosis that consists of unusual cutaneous sebaceous neoplasm, with or without kerathoacantomas and one or more low-grade visceral malignancies, with or without colonic polyps, in the absence of other predisposing factors. This chapter presents a review of the principal clinical and genetic findings in this syndrome and discusses its relation with Lynch sy

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Author information

Authors and Affiliations

  1. Dermatology Service Hospital General, Universitario Morales Meseguer, Murcia, Spain

    Pedro Mercader

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  1. Pedro Mercader
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Editor information

Editors and Affiliations

  1. School of Science and Technology, Nottingham Trent University, Nottingham, UK

    Shamim I. Ahmad BSc, MSc, PhD

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Mercader, P. (2010). Muir-Torre Syndrome. In: Ahmad, S.I. (eds) Diseases of DNA Repair. Advances in Experimental Medicine and Biology, vol 685. Springer, New York, NY. https://doi.org/10.1007/978-1-4419-6448-9_17

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