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Disease Subsets in Clinical Practice

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Scleroderma

Abstract

Systemic sclerosis is a heterogeneous disease with a varied clinical presentation and disease course. Classification is vital to grouping patients for clinical and research purposes. This chapter discusses the importance of classification systems, the currently accepted cutaneous-based classification of patients with an emphasis on staging of disease, and a combined cutaneous-serologic classification system. Patient profiles are presented.

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Authors and Affiliations

  1. Department of Medicine, Division of Rheumatology and Clinical Immunology, University of Pittsburgh Medical Center, Pittsburgh, PA, USA

    Robyn T. Domsic MD, MPH & Thomas A. Medsger Jr. MD

Authors
  1. Robyn T. Domsic MD, MPH
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  2. Thomas A. Medsger Jr. MD
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Corresponding author

Correspondence to Robyn T. Domsic MD, MPH .

Editor information

Editors and Affiliations

  1. Feinberg School of Medicine, Northwestern University, E. Huron Street 240, Chicago, 60611-2909, Illinois, USA

    John Varga

  2. Royal Free and University College, Medical School, University College London, Rowland Street, London, NW3 2PF, United Kingdom

    Christopher P. Denton

  3. School of Medicine, Div. Rheumatology, Johns Hopkins University, Eastern Avenue 5200, Baltimore, 21224, Maryland, USA

    Fredrick M. Wigley

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Domsic, R.T., Medsger, T.A. (2012). Disease Subsets in Clinical Practice. In: Varga, J., Denton, C., Wigley, F. (eds) Scleroderma. Springer, Boston, MA. https://doi.org/10.1007/978-1-4419-5774-0_6

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  • DOI: https://doi.org/10.1007/978-1-4419-5774-0_6

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  • Publisher Name: Springer, Boston, MA

  • Print ISBN: 978-1-4419-5773-3

  • Online ISBN: 978-1-4419-5774-0

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