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History and Diagnosis

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Behçet’s Syndrome

Abstract

Behçet’s syndrome, named after Hulusi Behçet Professor of Dermatology in Istanbul who described the “triple symptom complex” in 1937, is a multisystem, immunologically medicated vasculopathy. The principal clinical features are orogenital aphthous ulceration, uveitis, with or without hypopyon and retinal vasculitis and skin lesions including erythema nodosum and acneiform pustules. Inflammatory arthritis, arterial and venous occlusion and arterial aneurysms, gastrointestinal and neurological lesions also occur.

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Authors and Affiliations

  1. Department of Rheumatology, The Royal London Hospital, London, E1 1BB, UK

    Colin G. Barnes

  2. Department of Rheumatology, Barts and The London School of Medicine, Queen Mary University of London, London, UK

    Colin G. Barnes

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  1. Hospital for Joint Diseases, Behçet's Syndrome Center, NYU Medical Center, East 20th Street 246, New York, 10003, New York, USA

    Yusuf Yazıcı

  2. , Department of Medicine, University of Istanbul, Istanbul, 34452, Turkey

    Hasan Yazıcı

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Barnes, C.G. (2010). History and Diagnosis. In: Yazıcı, Y., Yazıcı, H. (eds) Behçet’s Syndrome. Springer, New York, NY. https://doi.org/10.1007/978-1-4419-5641-5_2

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