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Congenital Malformations of the Ear

Chapter

Abstract

Malformations affecting the ear encompass a wide spectrum of clinical entities. Interestingly, 50 % of all congenital malformations of the head and neck involve the ear. These malformations may present themselves as cosmetic and/or functional defects and can occur in isolation or as part of a constellation of features that define various associations and syndromes. They can affect the outer, middle, and/or inner ear, frequently in combination. The embryologic development of the outer and middle ear differs from that of the inner ear; this is reflected in the clinical presentation of ear malformations and forms the basis for many of the classification systems employed in clinical practice. This chapter reviews the embryology of the ear as well as the diagnosis and management of the most common malformations.

Keywords

Auricular atresia Microtia Congenital cholesteatoma Common cavity malformations Cochlear malformations 

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Copyright information

© Springer Science+Business Media New York 2014

Authors and Affiliations

  • Nael M. Shoman
    • 1
  • Ravi N. Samy
    • 2
  • Daniel I. Choo
    • 3
  1. 1.Division of Otolaryngology – Head and Neck Surgery, Department of SurgerySt. Paul’s HospitalSaskatoonCanada
  2. 2.Department of Otolaryngology Head and Neck SurgeryUniversity Hospital/University of CincinnatiCincinnatiUSA
  3. 3.Division of Pediatric Otolaryngology, Department of Otolaryngology Head and Neck SurgeryCincinnati Children’s Hospital Medical CenterCincinnatiUSA

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