L’hermitte–Duclos Disease and Cowden Disease
L’hermitte–Duclos disease (LDD) also known as dysplastic cerebellar gangliocytoma is a rare slowly enlarging cerebellar mass lesion composed of dysplastic ganglion cells. It has features of both hamartoma and benign neoplasm (WHO grade I). The exact incidence is unknown although most reports indicate that this is a rare condition. In the cerebellum, no cases of gangliocytoma have been reported except in the context of LDD.
KeywordsL’hermitte–Duclos disease Dysplastic gangliocytoma of the cerebellum Cowden disease
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